Beyond the Classic Distal Pattern: Proximal Upper Limb Monomelic Amyotrophy in Hirayama Disease
Sanaullah Mudassir1*, Abhay Ranjan2, Keshaw Kumar3, Ankit Panjwani4, Kanhaiya Raj1
1Department of Neurology, JP Medanta Superspeciality Hospital, Patna, India.
2Department of Neurology, IGIMS, Patna, India.
3Department of Radiology, JP Medanta Superspeciality Hospital, Patna, India.
4Department of Neurology, GMC, Nagpur, India.
*Corresponding Author: Dr. Sanaullah Mudassir, Senior Consultant Neurology, JP Medanta Superspeciality Hospital, Patna, India.
DOI: https://doi.org/10.58624/SVOANE.2026.07.023
Received: July 02, 2026
Published: August 04, 2026
Citation: Mudassir S, Ranjan A, Kumar K, Panjwani A, Raj K. Beyond the Classic Distal Pattern: Proximal Upper Limb Monomelic Amyotrophy in Hirayama Disease. SVOA Neurology 2026, 7:4, 160-162. doi.org/10.58624/SVOANE.2026.07.023
Abstract
Hirayama disease (HD) is, a benign lower motor neuron disease, characterized by unilateral weakness and wasting of distal upper limb in young adults. We herein report a case of atypical presentation of HD with proximal unilateral upper limb involvement.
Keywords: Hirayama Disease, Proximal, Monomelic Amyotrophy, Cervical Spine, Flexion
